Amyloid nephrosis

Familial renal amyloidosis
This condition is inherited in an autosomal dominant manner
Classification and external resources
Specialty	endocrinology
ICD-10	E85.0
ICD-9-CM	277.3
OMIM	105200
DiseasesDB	33335
eMedicine	med/3379
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Familial renal amyloidosis (or familial visceral amyloidosis, or hereditary amyloid nephropathy) is a form of amyloidosis primarily presenting in the kidney.

It is associated most commonly with congenital mutations in the fibrinogen alpha chain and classified as a dysfibrinogenemia (see Hereditary Fibrinogen Aα-Chain Amyloidosis). and, less commonly, with congenital mutations in apolipoprotein A1 and lysozyme.

It is also known as "Ostertag" type, after B. Ostertag, who characterized it in 1932 and 1950.

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